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第十章 结缔组织病
Connective Tissue Diseases
系统性红斑狼疮 Systemic Lupus Erythematosus,SLE
是侵犯皮肤和全身多脏器的一种自身免疫性疾病。
诊断要点:
多见于中青年女性。面部有蝶形红斑,手、足可有充血或出血斑,常伴雷诺征。患者光敏感,有肌肉、关节症状。可侵犯肾脏、心脏、肺脏和中枢神经系统,严重者威胁生命。实验室检查抗核抗体、Sm抗体等阳性。血白细胞总数低,尿中可有蛋白。
治疗要点:
应卧床休息,避免日光照晒。系统用糖皮质激素和/或免疫抑制剂,全身对症、支持治疗。
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-1_13914.jpg?sign=1739437654-I9UQrDffbozJSYWhLSlzjgnBqbkV53Lx-0-091f2f452fb22ec7a33808146a72b5b8)
图10-1-1 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-2_13912.jpg?sign=1739437654-XmfOqube9SN7MFqdRarzYcpnhryAzTbL-0-3de7890e5756fb20469c855ef667560f)
图10-1-2 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-3_13916.jpg?sign=1739437654-cwaFu6K0bRabZzJUh6Jz2Yt7Bgm3dlov-0-fae409dbf052f84339d39cac95aef8a7)
图10-1-3 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-4_13915.jpg?sign=1739437654-1dCLgIPpDnqQz7qDVeZxY6CrtvyoSawH-0-bb22a074b5eafff261b9c5d073de248e)
图10-1-4 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-5_13913.jpg?sign=1739437654-M01BlFEa4kf58kbfeC8vBV1TS9tIPmNs-0-ba8bd1c2f8d7d18db01d0b268ddfa5a6)
图10-1-5 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-6_13918.jpg?sign=1739437654-kvT08AcVw3V7EHbGVWNYKQJBaFz69xce-0-ff540ac40dee456a0c65a4949e53f7d6)
图10-1-6 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-7_13919.jpg?sign=1739437654-iDYD38BEA5HUpgXNI2XR11FhO0k4wJBN-0-3185b0484094569e154630b8929dd814)
图10-1-7 系统性红斑狼疮