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第十章 结缔组织病
Connective Tissue Diseases
系统性红斑狼疮 Systemic Lupus Erythematosus,SLE
是侵犯皮肤和全身多脏器的一种自身免疫性疾病。
诊断要点:
多见于中青年女性。面部有蝶形红斑,手、足可有充血或出血斑,常伴雷诺征。患者光敏感,有肌肉、关节症状。可侵犯肾脏、心脏、肺脏和中枢神经系统,严重者威胁生命。实验室检查抗核抗体、Sm抗体等阳性。血白细胞总数低,尿中可有蛋白。
治疗要点:
应卧床休息,避免日光照晒。系统用糖皮质激素和/或免疫抑制剂,全身对症、支持治疗。
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-1_13914.jpg?sign=1739422117-Z9HI1e5YltRuTu0QyQmMn3oN5FYrDwvo-0-c084ec0504e37127a002175c71ccb59b)
图10-1-1 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-2_13912.jpg?sign=1739422117-ogOXx2mi6VlBE8Tri9BtDq1GNbHctFI7-0-b78e16da4276adde158e47df8d7336e7)
图10-1-2 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-3_13916.jpg?sign=1739422117-iIYRdVmNw8O02xXSdmR56jyRdYz2dVBB-0-feec1e2a36470e8b6f597d7fc7557410)
图10-1-3 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-4_13915.jpg?sign=1739422117-pxFi8bGKEWgMtJcE6BML8Xvr2J3C4fxL-0-57474aa7094e1688dd31665b5c900b61)
图10-1-4 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-5_13913.jpg?sign=1739422117-SmUXv8tr8YDppTPEmGGpXBRD8Mlkk3p9-0-2e7d2439d1b9e8a253b10756e37cb223)
图10-1-5 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-6_13918.jpg?sign=1739422117-Iprx0a4Mevjc78WupAXXAD8B2xBawaxo-0-3f9434d2ee20b9087412f0fd397f7932)
图10-1-6 系统性红斑狼疮
![](https://epubservercos.yuewen.com/2D47EB/21846772801639806/epubprivate/OEBPS/Images/P10-1-7_13919.jpg?sign=1739422117-42V27aunprefqaYfI1taNh7gSCJNqhKq-0-2b018bdc586f4ee84a3cf0b5336f8527)
图10-1-7 系统性红斑狼疮